05232022Mon
Last updateWed, 09 Mar 2022 4am

Insidious malignant triton tumor of the chest wall with late flare-up

Jeng-Yuan Wua, b, Lai-Fa Sheub, c, Chao-Yuan Yaod

a Department of Thoracic Surgery, Taichung Tzu Chi Hospital, Buddhist Tzu Chi Medical Foundation, Taichung, Taiwan
b School of Medicine, Tzu Chi University, Hualien, Taiwan
c Department of Pathology, Taichung Tzu Chi Hospital, Buddhist Tzu Chi Medical Foundation, Taichung, Taiwan
d Department of Hematology–Oncology, Taichung Tzu Chi Hospital, Buddhist Tzu Chi Medical Foundation, Taichung, Taiwan

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Open Access funded by Buddhist Compassion Relief Tzu Chi Foundation


Abstract

Malignant triton tumor is a rare malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation. Most of these tumors are located in the head, neck, and extremities, and about half of cases are associated with neurofibromatosis type 1 featuring cafe-au-lait spots or cutaneous neurofibromas. We present a 76-year-old man with an insidious chest wall tumor with late progressive painful enlargement and pleural and pulmonary involvement. Complete resection of the affected thoracic wall as well as single separate lesions in the parietal pleura and left upper lung was carried out. The pathological examination confirmed that it was a malignant triton tumor. The patient received adjuvant chemoradiotherapy but eventually succumbed to disease relapse and distant metastases 6 months after the surgery.

Keywords

Chest wall tumor; Malignant peripheral nerve sheath tumor; Malignant triton tumor


 

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